Neurologic bases of hearing impairment

Project Details

There are a number of common hearing disorders which specifically affect the auditory nerve and central neural pathways rather than the ear itself.  These abnormalities (which are broadly termed "auditory neuropathies"), can involve a range of different mechanisms and sites-of-lesion. The aims of this research are to explore the processes underlying auditory neuropathy, to determine their functional (listening and communication)consequences and to develop targeted remediation strategies.


  • Donella Chisari, Tutor (PhD Candidate)
  • Julien Zanin, Tutor (PhD Candidate)
  • Bryony Nayagam, Senior Lecurer
  • Collaborators

    • Centre for Eye Research Australia (CERA)
    • Bruce Lefroy Centre for Genetic Health Research
    • Murdoch Childrens Research Institute (MCRI)
    • Friedreich Ataxia Research Alliance – Clinical Network
    • Florey Neurosciences Institute
    • Alfred Hospital – Dept of Neuroscience
    • Royal Victorian Eye & Ear Hospital
    • Bionics Institute
    • A/Prof Alan Connelly (Melbourne Brain Centre)


    • The HEARing Cooperative Research Centre
    • Jack Brockhoff Foundation
    • Collier Foundation
    • Deafness Foundation

    Research Opportunities

    This research project is available to PhD students to join as part of their thesis.
    Please contact the Research Group Leader to discuss your options.

    Research Publications

    Rance, G., Beer, D.E., Cone-Wesson, B., Shepherd, R.K., King, A., Rickards, F.W., & Clark, G.M. (1999).  Clinical findings for a group of infants and young children with auditory neuropathy.  Ear & Hearing, 20 (3), 238-252.

    Rance, G., Fava, R., Baldock, H., Chong, A., Barker, E., Corben, L. & Delatycki, M. (2008).  Speech perception ability in individuals with Friedreich ataxia.  Brain, 131, 2002-2012.

    Rance G, Ryan MM, Bayliss K, Gill K, O’Sullivan C, Whitechurch M. (2012).  Auditory Function in Children with Charcot-Marie-Tooth Disease.  Brain. 135, 1412-1422.

    Rance G, Starr A.  (2015).  Pathophysiological Mechanisms and Functional Hearing Consequences of Auditory Neuropathy.  Brain 138:3141-3158.

    Research Group

    Identification and Management of Hearing Disorders

    Faculty Research Themes


    School Research Themes

    Neuroscience & Mental Health

    Key Contact

    For further information about this research, please contact the research group leader.

    Department / Centre

    Audiology and Speech Pathology

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