Neurologic bases of hearing impairment
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Principle Investigator
Associate Professor Gary Rance03 9035 5342
Project Details
There are a number of common hearing disorders which specifically affect the auditory nerve and central neural pathways rather than the ear itself. These abnormalities (which are broadly termed "auditory neuropathies"), can involve a range of different mechanisms and sites-of-lesion. The aims of this research are to explore the processes underlying auditory neuropathy, to determine their functional (listening and communication)consequences and to develop targeted remediation strategies.
Researchers
Collaborators
- Centre for Eye Research Australia (CERA)
- Bruce Lefroy Centre for Genetic Health Research
- Murdoch Childrens Research Institute (MCRI)
- Friedreich Ataxia Research Alliance – Clinical Network
- Florey Neurosciences Institute
- Alfred Hospital – Dept of Neuroscience
- Royal Victorian Eye & Ear Hospital
- Bionics Institute
- A/Prof Alan Connelly (Melbourne Brain Centre)
Funding
- The HEARing Cooperative Research Centre
- Jack Brockhoff Foundation
- Collier Foundation
- Deafness Foundation
Research Publications
Rance, G., Beer, D.E., Cone-Wesson, B., Shepherd, R.K., King, A., Rickards, F.W., & Clark, G.M. (1999). Clinical findings for a group of infants and young children with auditory neuropathy. Ear & Hearing, 20 (3), 238-252.
Rance, G., Fava, R., Baldock, H., Chong, A., Barker, E., Corben, L. & Delatycki, M. (2008). Speech perception ability in individuals with Friedreich ataxia. Brain, 131, 2002-2012.
Rance G, Ryan MM, Bayliss K, Gill K, O’Sullivan C, Whitechurch M. (2012). Auditory Function in Children with Charcot-Marie-Tooth Disease. Brain. 135, 1412-1422.
Rance G, Starr A. (2015). Pathophysiological Mechanisms and Functional Hearing Consequences of Auditory Neuropathy. Brain 138:3141-3158.